Substance Name: Taliglucerase alfa [USAN:INN]
RN: 37228-64-1
UNII: N69L6LM4QU
Note
- A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in GAUCHER DISEASE. EC 3.2.1.45.
Molecular Formula
- Unspecified
Classification Code
- Treatment of Gaucher Disease
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Names and Synonyms
Name of Substance
- Glucosylceramidase
- Taliglucerase alfa [USAN:INN]
MeSH Heading
- Glucosylceramidase
Synonyms
- Acid beta-glucosidase
- beta-D-Glucocerebrosidase
- beta-Glucosylceramidase
- Ceramide glucosidase
- Cerebroside beta-glucosidase
- Elelyso
- Glucocerebrosidase
- Glucocerebroside beta-glucosidase
- Glucose cerebrosidase
- Glucosylceramide beta-glucosidase
- Glucosylcerebrosidase
- Glucosylsphingosine beta-D-glucosidase
- Glucosylsphingosine beta-glucosidase
- prGCD
- Taliglucerase alfa
- UNII-N69L6LM4QU
- Uplyso
Systematic Name
- Ceramidase, glucosyl-
Registry Numbers
CAS Registry Number
- 37228-64-1
FDA UNII
- N69L6LM4QU
System Generated Number
- 0037228641