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Substance Name: Argininosuccinate Synthase
RN: 9023-58-9


  • An enzyme of the urea cycle that catalyzes the formation of argininosuccinic acid from citrulline and aspartic acid in the presence of ATP. Absence or deficiency of this enzyme causes the metabolic disease CITRULLINEMIA in humans. EC
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Names and Synonyms

Name of Substance

  • Argininosuccinate Synthase

MeSH Heading

  • Argininosuccinate Synthase


  • Argininosuccinate Synthetase
  • Synthase, argininosuccinate
  • Synthetase, argininosuccinate

Systematic Name

  • L-Citrulline:L-aspartate ligase (AMP-forming)

Registry Numbers

CAS Registry Number

  • 9023-58-9

System Generated Number

  • 0009023589